2. OBJECTIVES
?Define imperforated anus
?Explain the causes of imperforated
anus
?Explain the types of imperforated anus
?Describe the therapeutic management
?Describe the nursing management
3. DEFINITION
?Imperforate anus or anal atresia is a
congenital anorectal malformation
(ARM) where a normal anal opening is
absent at birth.
6. Pathophysiology
?Anorectal malformations occur during
the 8 to 12 weeks of fetal gestation due
to the failure to complete the
development of the hindgut.
?There is impaired septation, and the
cloacal membrane is usually found to
be short in its dorsal part; thus, the
hindgut retains its attachment to the
sinus urogenitalis.
7. CAUSES
? The causes are not known. However the
occurrence is 1 in every 5,000 live births. It
is common in males and no racial evidence
has been documented
? Studies have also shown that a family with a
previous imperforated anus of a sibling, they
are more likely to get the condition, however,
there is no evidence to determine genetic
predisposition
8. CLINICAL PRESENTATIONS
? Failure to pass meconium during the first 24 hours
of birth.
? Abdominal distention
? Examine the perineum thoroughly at birth and after
24 hours.
? There is no anal opening or there could be a small
depression (an anal pit).
9. Clinical presentation ctd
NOTE:
? The presence of a small orifice, not at the normal
position of the anus, may indicate a perineal
fistula.
? This defect is usually present anterior to the anal
sphincter complex.
? There may be a fistula to the genitourinary tract if
stool is noted coming out of the urethra or vagina
instead of the anus.
10. TYPES OF IMPERFORATED ANUS
LOW TYPE
? Opening is present but either in the wrong position
or its covered by a membrane
HIGH TYPE
? No opening is present
11. MANAGEMENT
ASSESMENT
? Inspect the perineum for location and size of the
anal opening
? If no opening, careful inspection of the genital
urinary should be done to exclude any other
openings
? In males the opening may be found in recto
prostatic or recto urinary
? In females the fistula may open at the posterior
vestibule or vaginaly
12. THERAPEUTIC MANAGEMENT
management depends on type
LOW TYPE
?Surgery is done to open the membrane
?Dilatation of the opening is also done
?Surgery to reconstruct the anus is done
13. Management cont´..
HIGH TYPE
?First surgery is done immediately to
create a colostomy and mucosa fistula
?Ends of the bowel are brought out
through the stomach to create one or 2
openings(stoma) then a colostomy bag
is connected to collect the stools
through the stoma
14. Management cont´
?Second surgery is done 3 to 6 months
later.
?This is done to rebuild the anal opening
?Third surgery is done 2 t0 3 months
later.
?This is aimed at closing the colostomy
and the mucus fistula, and the bowels
are reconstructed
15. NURSING MANAGEMENT
Infection prevention.
? Teach the mother to keep the area around the
colostomy clean with soap and water and to
diaper the baby in the usual way;
? monitor white blood cell (WBC) count to rule out
infection; and
? wash hands before and after handling the baby and
teach the mother to wash hands before contact
with the baby and between procedures with the
baby.
16. Nursing management cont´.
? Protect skin integrity. A protective ointment is
useful to protect the skin around the
colostomy;
? monitor site of impaired tissue integrity at
least once daily for color changes, redness,
swelling, warmth, pain, or other signs of
infection; and
? keep a sterile dressing technique during
wound care.
17. Nsg management cont´.
Restore balanced fluid volume.
? Administer parenteral fluids as prescribed;
? consider the need for an IV fluid challenge
with an immediate infusion of fluids for
patients with abnormal vital signs;