The document discusses vein of Galen malformations, which develop during fetal development when the vein of Markowski fails to regress and drains abnormally into the vein of Galen. It can cause high-output heart failure in newborns. The malformations are classified based on their blood supply and connections. Treatment options aim to reduce blood flow through the malformation via embolization, resection, or radiosurgery in order to improve the generally poor prognosis.
2. PRESENTATION
AS CCF IN THE FIRST WEEK OF LIFE AND HAVE
POOR PROGNOSIS
3. VEIN OF GALEN
The congenital malformation develops during
weeks 6-11 of fetal development as a
persistent embryonic prosencephalic vein of
Markowski thus, VGAM is actually a
misnomer.
The vein of Markowski actually drains into the
vein of Galen.
4. It can produce hydrocephalus if it obstructs
the sylvian aqueduct
7. True VOG ARE FED FROM
ANTERIOR CHOROIDAL
MEDIAL AND LATERAL CHOROIDAL
MESENCEPHALIC
PERICALLOSAL VESSELS
8. TYPES OF VEIN OF GALEN
MALFORMATION
PURE INTERNAL FISTULA
FISTULA BETWEEN THALAMOPERFORATORS
AND VEIN OF GALEN
MIXED FORM(MOST COMMON TYPE)
PLEXIFORM TYPE
11. CLASSIFICATION
YASARGILL CLASSIFICATION
TYPE I PURE CISTERNAL CONNECTION
BETWEEN VOG AND PERICALLOSAL /
POSTERIOR CEREBRAL
TYPE II - MULTIPLE FISTULUS CONNECTION
BETWEEN THALAMOPERFORATORS AND VOG
12. TYPE III
HIGH FLOW MIXED TYPE I AND TYPE II
TYPE IV
PARENCHYMAL AVM WITH DRAINAGE