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VEIN OF GALEN MALFORMATION
 PRESENTATION
 AS CCF IN THE FIRST WEEK OF LIFE AND HAVE
POOR PROGNOSIS
VEIN OF GALEN
 The congenital malformation develops during
weeks 6-11 of fetal development as a
persistent embryonic prosencephalic vein of
Markowski thus, VGAM is actually a
misnomer.
 The vein of Markowski actually drains into the
vein of Galen.
 It can produce hydrocephalus if it obstructs
the sylvian aqueduct
Vein of galen malformation
Vein of galen malformation
 True VOG ARE FED FROM
 ANTERIOR CHOROIDAL
 MEDIAL AND LATERAL CHOROIDAL
 MESENCEPHALIC
 PERICALLOSAL VESSELS
TYPES OF VEIN OF GALEN
MALFORMATION
 PURE INTERNAL FISTULA
 
 FISTULA BETWEEN THALAMOPERFORATORS
AND VEIN OF GALEN
 MIXED FORM(MOST COMMON TYPE)
 PLEXIFORM TYPE
CLINICAL FEATURES
 RESPIRATORY DISTRESS
 REFUSAL OF FEED
 HYDROCEPHALUS  SUNSET SIGN
 CYANOSIS
 SEIZURES
CLASSIFICATION
 LASJAUNIAS CLASSIFICATION
 CHOROIDAL
 MURAL
CLASSIFICATION
 YASARGILL CLASSIFICATION
 TYPE I  PURE CISTERNAL CONNECTION
BETWEEN VOG AND PERICALLOSAL /
POSTERIOR CEREBRAL
 TYPE II - MULTIPLE FISTULUS CONNECTION
BETWEEN THALAMOPERFORATORS AND VOG
 TYPE III
 HIGH FLOW MIXED TYPE I AND TYPE II
TYPE IV
PARENCHYMAL AVM WITH DRAINAGE
PROGNOSIS
 POOR
TREATMENT
 OPTION COMPRISES OF
 EMBOLIZATION
 RESECTION
 RADIOSURGERY

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Vein of galen malformation

  • 1. VEIN OF GALEN MALFORMATION
  • 2. PRESENTATION AS CCF IN THE FIRST WEEK OF LIFE AND HAVE POOR PROGNOSIS
  • 3. VEIN OF GALEN The congenital malformation develops during weeks 6-11 of fetal development as a persistent embryonic prosencephalic vein of Markowski thus, VGAM is actually a misnomer. The vein of Markowski actually drains into the vein of Galen.
  • 4. It can produce hydrocephalus if it obstructs the sylvian aqueduct
  • 7. True VOG ARE FED FROM ANTERIOR CHOROIDAL MEDIAL AND LATERAL CHOROIDAL MESENCEPHALIC PERICALLOSAL VESSELS
  • 8. TYPES OF VEIN OF GALEN MALFORMATION PURE INTERNAL FISTULA FISTULA BETWEEN THALAMOPERFORATORS AND VEIN OF GALEN MIXED FORM(MOST COMMON TYPE) PLEXIFORM TYPE
  • 9. CLINICAL FEATURES RESPIRATORY DISTRESS REFUSAL OF FEED HYDROCEPHALUS SUNSET SIGN CYANOSIS SEIZURES
  • 11. CLASSIFICATION YASARGILL CLASSIFICATION TYPE I PURE CISTERNAL CONNECTION BETWEEN VOG AND PERICALLOSAL / POSTERIOR CEREBRAL TYPE II - MULTIPLE FISTULUS CONNECTION BETWEEN THALAMOPERFORATORS AND VOG
  • 12. TYPE III HIGH FLOW MIXED TYPE I AND TYPE II TYPE IV PARENCHYMAL AVM WITH DRAINAGE
  • 14. TREATMENT OPTION COMPRISES OF EMBOLIZATION RESECTION RADIOSURGERY